Extraventricular neurocytoma

Authors

Keywords:

diplopia, neoplasms, neurocytoma

Abstract

Introduction: Extraventricular neurocytoma is a rare neuronal tumor located outside the ventricular system. It can present at any age and manifests with nonspecific neurological symptoms (seizures or focal deficits). Due to its low incidence, the literature on extraventricular neurocytoma is limited, so describing clinical cases contributes to improving understanding and management of this entity.

Objective: To describe the clinical, imaging, histopathological, and therapeutic characteristics of a case of extraventricular neurocytoma treated by transphenoidal endonasal approach.

Clinical case:  A 65-year-old Caucasian male patient with a history of type 2 diabetes mellitus presented with progressive dizziness associated with changes in head position, horizontal binocular diplopia, constant tinnitus in the left ear, and gait instability. He occasionally experienced episodes of holocranial headache, which resolved with analgesics and were not accompanied by vomiting. Neurological examination revealed bilateral paresis of the sixth cranial nerve. Computed tomography revealed a hyperdense image in the clivus projection surrounding both internal carotid arteries. A transsphenoidal endoscopic endonasal approach was performed, and tumor excision was performed, with favorable patient outcome.

Conclusions: Extraventricular neurocytoma is a rare tumor of the central nervous system with a favorable prognosis after complete resection. Further studies are needed to define optimal therapeutic protocols because, despite being a benign lesion, it affects the patient's quality of life.

References

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Published

2025-11-01

How to Cite

1.
Jardinez Hinojosa Y, Rojas Manresa JL, Nueva Matos J, Forcelledo Gómez M, González Orlandi Y, Rodríguez Borges W, et al. Extraventricular neurocytoma. Invest Medicoquir [Internet]. 2025 Nov. 1 [cited 2025 Dec. 27];17(1):e1004. Available from: https://revcimeq.sld.cu/index.php/imq/article/view/1004

Issue

Vol. 17 No. 1 (2025): in progress

Section

Case presentation

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Copyright (c) 2025 Yanely Jardinez Hinojosa, Jorge Luis Rojas Manresa, Jorge Nueva Matos, Maibelis Forcelledo Gómez, Yvei González Orlandi , Wendolin Rodríguez Borges, Mayren Sotomayor González, Mercedes Rita Salinas Olivares

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